W. Chang, C. Chen, C. Liu, M. Chen, H. Wang, C. Lin
Systemic sclerosis is a multisystem autoimmune rheumatic disorder characterized by fibrosis in the skin and internal organs but rarely with hepatic or brain involvement. Reversible posterior leukoencephalopathy syndrome is characterized by a unique pattern of brain vasogenic edema in the setting of neurotoxicity predominantly in the parietal and occipital regions. We report a case of systemic sclerosis associated with probable autoimmune hepatitis that progressed rapidly to reversible posterior leukoencephalopathy syndrome with loss of vision, seizures, and coagulopathy. Brain computed tomography showed faint low density in the bilateral occipital lobes and posterior parietal lobes with edematous change. Fortunately, the patients clinical condition considerably improved 2 days following the initiation of 100 mg intravenous hydrocortisone infusion.
Keywords:
Diff selection: Mark the radio boxes of the revisions to compare and hit enter or the button at the bottom. Legend: (cur) = difference with latest revision, (prev) = difference with preceding revision, m = minor edit.
Published on 15/05/17Submitted on 15/05/17
Licence: Other
Views 2Recommendations 0
Are you one of the authors of this document?